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Sildenafil in neonatal pulmonary hypertension due to impaired alveolarisation and plexiform pulmonary arteriopathy.

Chaudhari M, Vogel M, Wright C, Smith J, Haworth SG

Freeman Hospital, Newcastle upon Tyne, NE7 7DN, UK. milind.chaudhari@nuth.northy.nhs.uk

We report a case of severe pulmonary hypertension in a neonate associated with impaired alveolarisation and plexiform pulmonary arteriopathy. Treatment with oral sildenafil in addition to inhaled nitric oxide (NO) resulted in recovery from the pulmonary hypertensive crisis. Long term sildenafil therapy was associated with complete resolution of the pulmonary hypertension.

Published 24 October 2005 in Arch Dis Child Fetal Neonatal Ed, 90(6): F527-8.
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